Tipifarnib for Advanced Solid Tumors, Lymphoma & Histiocytic Disorders with HRAS Gene Alterations in Pediatrics
Active, Not Recruiting Phase 2 NCT04284774
Study Description
This trial studies the effectiveness of Tipifarnib in treating pediatric patients with advanced solid tumors, lymphomas, or histiocytic disorders. Tipifarnib works by blocking cancer cell growth and reducing tumor size in patients with a genetic alteration in HRAS gene. The trial is focused on determining the objective response rate (ORR; complete response + partial response) and the progression-free survival rate in these types of cancers. It also aims to obtain information on the drug's tolerability and evaluate other biomarkers as predictors of response to Tipifarnib. Patients receive Tipifarnib orally or through a nasogastric or gastric tube, with tumor disease evaluation throughout the trial. Blood specimen collections may also be required. After the treatment, patients are followed up.
Study Details
- Registry ID:
- NCT04284774
- Conditions:
- Malignant Solid Neoplasm, Recurrent Adrenal Gland Pheochromocytoma, Recurrent Ectomesenchymoma, Recurrent Ependymoma, Recurrent Ewing Sarcoma, Recurrent Hepatoblastoma, Recurrent Kidney Wilms Tumor, Recurrent Langerhans Cell Histiocytosis, Recurrent Malignant Germ Cell Tumor, Recurrent Malignant Glioma, Recurrent Medulloblastoma, Recurrent Melanoma, Recurrent Neuroblastoma, Recurrent Non-Hodgkin Lymphoma, Recurrent Osteosarcoma, Recurrent Peripheral Primitive Neuroectodermal Tumor, Recurrent Rhabdoid Tumor, Recurrent Rhabdoid Tumor of the Kidney, Recurrent Rhabdomyosarcoma, Recurrent Soft Tissue Sarcoma, Recurrent Thyroid Gland Carcinoma, Recurrent WHO Grade 2 Glioma, Refractory Adrenal Gland Pheochromocytoma, Refractory Ependymoma, Refractory Ewing Sarcoma, Refractory Hepatoblastoma, Refractory Langerhans Cell Histiocytosis, Refractory Malignant Germ Cell Tumor, Refractory Malignant Glioma, Refractory Medulloblastoma, Refractory Melanoma, Refractory Neuroblastoma, Refractory Non-Hodgkin Lymphoma, Refractory Osteosarcoma, Refractory Peripheral Primitive Neuroectodermal Tumor, Refractory Rhabdoid Tumor, Refractory Rhabdoid Tumor of the Kidney, Refractory Rhabdomyosarcoma, Refractory Soft Tissue Sarcoma, Refractory Thyroid Gland Carcinoma, Refractory WHO Grade 2 Glioma
- Phase:
- Phase 2
- Target Enrollment:
- 5 participants
- Start Date:
- Age Range:
- 1–21 years
- Healthy Volunteers:
- No
Study Locations (199 sites)
-
University Pediatric Hospital
San Juan, Puerto Rico, Puerto Rico -
University Pediatric Hospital
San Juan, Puerto Rico -
Eastern Maine Medical Center
Bangor, Maine, United States -
Massachusetts General Hospital Cancer Center
Boston, Massachusetts, United States -
Dana-Farber Cancer Institute
Boston, Massachusetts, United States -
Maine Children's Cancer Program
Scarborough, Maine, United States -
Rhode Island Hospital
Providence, Rhode Island, United States -
UMass Memorial Medical Center - University Campus
Worcester, Massachusetts, United States -
Stony Brook University Medical Center
Stony Brook, New York, United States -
Yale University
New Haven, Connecticut, United States -
Connecticut Children's Medical Center
Hartford, Connecticut, United States -
NYU Winthrop Hospital
Mineola, New York, United States -
NYU Langone Hospital - Long Island
Mineola, New York, United States -
The Steven and Alexandra Cohen Children's Medical Center of New York
New Hyde Park, New York, United States -
University of Miami Miller School of Medicine-Sylvester Cancer Center
Miami, Florida, United States -
Nicklaus Children's Hospital
Miami, Florida, United States -
Miami Cancer Institute
Miami, Florida, United States -
Memorial Regional Hospital/Joe DiMaggio Children's Hospital
Hollywood, Florida, United States -
Broward Health Medical Center
Fort Lauderdale, Florida, United States -
Saint Mary's Hospital
West Palm Beach, Florida, United States -
Saint Mary's Medical Center
West Palm Beach, Florida, United States -
Montefiore Medical Center - Moses Campus
Bronx, New York, United States -
Montefiore Medical Center - Moses Campus
The Bronx, New York, United States -
Dartmouth Hitchcock Medical Center/Dartmouth Cancer Center
Lebanon, New Hampshire, United States -
Dartmouth Hitchcock Medical Center
Lebanon, New Hampshire, United States -
New York Medical College
Valhalla, New York, United States -
Laura and Isaac Perlmutter Cancer Center at NYU Langone
New York, New York, United States -
NYP/Columbia University Medical Center/Herbert Irving Comprehensive Cancer Center
New York, New York, United States -
Memorial Sloan Kettering Cancer Center
New York, New York, United States -
NYP/Weill Cornell Medical Center
New York, New York, United States -
Hackensack University Medical Center
Hackensack, New Jersey, United States -
Children's Hospital of The King's Daughters
Norfolk, Virginia, United States -
Naval Medical Center - Portsmouth
Portsmouth, Virginia, United States -
Saint Peter's University Hospital
New Brunswick, New Jersey, United States -
Rutgers Cancer Institute of New Jersey-Robert Wood Johnson University Hospital
New Brunswick, New Jersey, United States -
Morristown Medical Center
Morristown, New Jersey, United States -
Children's Hospital of Philadelphia
Philadelphia, Pennsylvania, United States -
Saint Christopher's Hospital for Children
Philadelphia, Pennsylvania, United States -
East Carolina University
Greenville, North Carolina, United States -
Albany Medical Center
Albany, New York, United States -
Alfred I duPont Hospital for Children
Wilmington, Delaware, United States -
University of Vermont and State Agricultural College
Burlington, Vermont, United States -
Lehigh Valley Hospital-Cedar Crest
Allentown, Pennsylvania, United States -
Golisano Children's Hospital of Southwest Florida
Fort Myers, Florida, United States -
Virginia Commonwealth University/Massey Cancer Center
Richmond, Virginia, United States -
VCU Massey Comprehensive Cancer Center
Richmond, Virginia, United States -
University of Maryland/Greenebaum Cancer Center
Baltimore, Maryland, United States -
Sinai Hospital of Baltimore
Baltimore, Maryland, United States -
Johns Hopkins University/Sidney Kimmel Cancer Center
Baltimore, Maryland, United States -
AdventHealth Orlando
Orlando, Florida, United States -
Arnold Palmer Hospital for Children
Orlando, Florida, United States -
Nemours Children's Hospital
Orlando, Florida, United States -
MedStar Georgetown University Hospital
Washington, District of Columbia, United States -
Children's National Medical Center
Washington, District of Columbia, United States -
MedStar Georgetown University Hospital
Washington D.C., District of Columbia, United States -
Children's National Medical Center
Washington D.C., District of Columbia, United States -
National Institutes of Health Clinical Center
Bethesda, Maryland, United States -
Inova Fairfax Hospital
Falls Church, Virginia, United States -
Duke University Medical Center
Durham, North Carolina, United States -
UNC Lineberger Comprehensive Cancer Center
Chapel Hill, North Carolina, United States -
Geisinger Medical Center
Danville, Pennsylvania, United States -
Tampa General Hospital
Tampa, Florida, United States -
Saint Joseph's Hospital/Children's Hospital-Tampa
Tampa, Florida, United States -
Nemours Children's Clinic-Jacksonville
Jacksonville, Florida, United States -
Memorial Health University Medical Center
Savannah, Georgia, United States -
Johns Hopkins All Children's Hospital
Saint Petersburg, Florida, United States -
Johns Hopkins All Children's Hospital
Saint Petersburg, Florida, United States -
State University of New York Upstate Medical University
Syracuse, New York, United States -
University of Florida Health Science Center - Gainesville
Gainesville, Florida, United States -
UF Health Cancer Institute - Gainesville
Gainesville, Florida, United States -
Prisma Health Richland Hospital
Columbia, South Carolina, United States -
Wake Forest University Health Sciences
Winston-Salem, North Carolina, United States -
Carolinas Medical Center/Levine Cancer Institute
Charlotte, North Carolina, United States -
Novant Health Presbyterian Medical Center
Charlotte, North Carolina, United States -
University of Rochester
Rochester, New York, United States -
West Virginia University Healthcare
Morgantown, West Virginia, United States -
BI-LO Charities Children's Cancer Center
Greenville, South Carolina, United States -
Children's Hospital of Pittsburgh of UPMC
Pittsburgh, Pennsylvania, United States -
Roswell Park Cancer Institute
Buffalo, New York, United States -
Mission Hospital
Asheville, North Carolina, United States -
Children's Healthcare of Atlanta - Arthur M Blank Hospital
Atlanta, Georgia, United States -
Children's Healthcare of Atlanta - Egleston
Atlanta, Georgia, United States -
Children's Hospital Medical Center of Akron
Akron, Ohio, United States -
East Tennessee Childrens Hospital
Knoxville, Tennessee, United States -
Rainbow Babies and Childrens Hospital
Cleveland, Ohio, United States -
Cleveland Clinic Foundation
Cleveland, Ohio, United States -
Nationwide Children's Hospital
Columbus, Ohio, United States -
T C Thompson Children's Hospital
Chattanooga, Tennessee, United States -
Sacred Heart Hospital
Pensacola, Florida, United States -
University of Kentucky/Markey Cancer Center
Lexington, Kentucky, United States -
Children's Hospital of Alabama
Birmingham, Alabama, United States -
Dayton Children's Hospital
Dayton, Ohio, United States -
Cincinnati Children's Hospital Medical Center
Cincinnati, Ohio, United States -
Wayne State University/Karmanos Cancer Institute
Detroit, Michigan, United States -
Children's Hospital of Michigan
Detroit, Michigan, United States -
ProMedica Toledo Hospital/Russell J Ebeid Children's Hospital
Toledo, Ohio, United States -
Beaumont Children's Hospital-Royal Oak
Royal Oak, Michigan, United States -
Corewell Health Children's
Royal Oak, Michigan, United States -
C S Mott Children's Hospital
Ann Arbor, Michigan, United States -
Norton Children's Hospital
Louisville, Kentucky, United States -
The Children's Hospital at TriStar Centennial
Nashville, Tennessee, United States -
Vanderbilt University/Ingram Cancer Center
Nashville, Tennessee, United States -
Michigan State University Clinical Center
East Lansing, Michigan, United States -
Michigan State University
East Lansing, Michigan, United States -
Riley Hospital for Children
Indianapolis, Indiana, United States -
Ascension Saint Vincent Indianapolis Hospital
Indianapolis, Indiana, United States -
Saint Vincent Hospital and Health Care Center
Indianapolis, Indiana, United States -
Children's Hospital New Orleans
New Orleans, Louisiana, United States -
Ochsner Medical Center Jefferson
New Orleans, Louisiana, United States -
Bronson Methodist Hospital
Kalamazoo, Michigan, United States -
University of Mississippi Medical Center
Jackson, Mississippi, United States -
Helen DeVos Children's Hospital at Spectrum Health
Grand Rapids, Michigan, United States -
Corewell Health Grand Rapids Hospitals - Helen DeVos Children's Hospital
Grand Rapids, Michigan, United States -
Saint Jude Children's Research Hospital
Memphis, Tennessee, United States -
Lurie Children's Hospital-Chicago
Chicago, Illinois, United States -
University of Illinois
Chicago, Illinois, United States -
University of Chicago Comprehensive Cancer Center
Chicago, Illinois, United States -
Loyola University Medical Center
Maywood, Illinois, United States -
Children's Hospital of Wisconsin
Milwaukee, Wisconsin, United States -
Southern Illinois University School of Medicine
Springfield, Illinois, United States -
Cardinal Glennon Children's Medical Center
Saint Louis, Missouri, United States -
Washington University School of Medicine
Saint Louis, Missouri, United States -
Mercy Hospital Saint Louis
Saint Louis, Missouri, United States -
Cardinal Glennon Children's Medical Center
Saint Louis, Missouri, United States -
Washington University School of Medicine
Saint Louis, Missouri, United States -
Mercy Hospital Saint Louis
Saint Louis, Missouri, United States -
Cardinal Glennon Children's Medical Center
St Louis, Missouri, United States -
Washington University School of Medicine
St Louis, Missouri, United States -
Mercy Hospital Saint Louis
St Louis, Missouri, United States -
Saint Jude Midwest Affiliate
Peoria, Illinois, United States -
OSF Children's Hospital of Illinois
Peoria, Illinois, United States -
Arkansas Children's Hospital
Little Rock, Arkansas, United States -
University of Wisconsin Carbone Cancer Center
Madison, Wisconsin, United States -
University of Wisconsin Carbone Cancer Center - University Hospital
Madison, Wisconsin, United States -
Baylor College of Medicine/Dan L Duncan Comprehensive Cancer Center
Houston, Texas, United States -
M D Anderson Cancer Center
Houston, Texas, United States -
UT MD Anderson Cancer Center
Houston, Texas, United States -
University of Iowa/Holden Comprehensive Cancer Center
Iowa City, Iowa, United States -
Marshfield Medical Center-Marshfield
Marshfield, Wisconsin, United States -
Driscoll Children's Hospital
Corpus Christi, Texas, United States -
Scott and White Memorial Hospital
Temple, Texas, United States -
Medical City Dallas Hospital
Dallas, Texas, United States -
UT Southwestern/Simmons Cancer Center-Dallas
Dallas, Texas, United States -
Dell Children's Medical Center of Central Texas
Austin, Texas, United States -
Children's Mercy Hospitals and Clinics
Kansas City, Missouri, United States -
Mayo Clinic in Rochester
Rochester, Minnesota, United States -
Blank Children's Hospital
Des Moines, Iowa, United States -
Cook Children's Medical Center
Fort Worth, Texas, United States -
Children's Hospital of San Antonio
San Antonio, Texas, United States -
Methodist Children's Hospital of South Texas
San Antonio, Texas, United States -
University of Texas Health Science Center at San Antonio
San Antonio, Texas, United States -
Children's Hospitals and Clinics of Minnesota - Minneapolis
Minneapolis, Minnesota, United States -
University of Minnesota/Masonic Cancer Center
Minneapolis, Minnesota, United States -
University of Oklahoma Health Sciences Center
Oklahoma City, Oklahoma, United States -
Children's Hospital and Medical Center of Omaha
Omaha, Nebraska, United States -
University of Nebraska Medical Center
Omaha, Nebraska, United States -
Sanford USD Medical Center - Sioux Falls
Sioux Falls, South Dakota, United States -
Covenant Children's Hospital
Lubbock, Texas, United States -
UMC Cancer Center / UMC Health System
Lubbock, Texas, United States -
Sanford Broadway Medical Center
Fargo, North Dakota, United States -
El Paso Children's Hospital
El Paso, Texas, United States -
Children's Hospital Colorado
Aurora, Colorado, United States -
Rocky Mountain Hospital for Children-Presbyterian Saint Luke's Medical Center
Denver, Colorado, United States -
Banner University Medical Center - Tucson
Tucson, Arizona, United States -
Banner Children's at Desert
Mesa, Arizona, United States -
Phoenix Childrens Hospital
Phoenix, Arizona, United States -
Primary Children's Hospital
Salt Lake City, Utah, United States -
University Medical Center of Southern Nevada
Las Vegas, Nevada, United States -
Sunrise Hospital and Medical Center
Las Vegas, Nevada, United States -
Alliance for Childhood Diseases/Cure 4 the Kids Foundation
Las Vegas, Nevada, United States -
Summerlin Hospital Medical Center
Las Vegas, Nevada, United States -
Rady Children's Hospital - San Diego
San Diego, California, United States -
Naval Medical Center -San Diego
San Diego, California, United States -
Loma Linda University Medical Center
Loma Linda, California, United States -
Children's Hospital of Orange County
Orange, California, United States -
City of Hope Comprehensive Cancer Center
Duarte, California, United States -
Kaiser Permanente Downey Medical Center
Downey, California, United States -
Miller Children's and Women's Hospital Long Beach
Long Beach, California, United States -
Children's Hospital Los Angeles
Los Angeles, California, United States -
Cedars Sinai Medical Center
Los Angeles, California, United States -
Mattel Children's Hospital UCLA
Los Angeles, California, United States -
Cedars-Sinai Medical Center
Los Angeles, California, United States -
Lundquist Institute for Biomedical Innovation at Harbor-UCLA Medical Center
Torrance, California, United States -
Saint Luke's Cancer Institute - Boise
Boise, Idaho, United States -
Valley Children's Hospital
Madera, California, United States -
Renown Regional Medical Center
Reno, Nevada, United States -
Providence Sacred Heart Medical Center and Children's Hospital
Spokane, Washington, United States -
University of California Davis Comprehensive Cancer Center
Sacramento, California, United States -
Lucile Packard Children's Hospital Stanford University
Palo Alto, California, United States -
UCSF Benioff Children's Hospital Oakland
Oakland, California, United States -
Kaiser Permanente-Oakland
Oakland, California, United States -
UCSF Medical Center-Mission Bay
San Francisco, California, United States -
Legacy Emanuel Children's Hospital
Portland, Oregon, United States -
Oregon Health and Science University
Portland, Oregon, United States -
Mary Bridge Children's Hospital and Health Center
Tacoma, Washington, United States -
Madigan Army Medical Center
Tacoma, Washington, United States -
Seattle Children's Hospital
Seattle, Washington, United States -
Kapiolani Medical Center for Women and Children
Honolulu, Hawaii, United States -
Providence Alaska Medical Center
Anchorage, Alaska, United States
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